2) hemophagocytic syndrome
噬血细胞综合征
1.
Study of early experimental indexes changes on hemophagocytic syndrome;
噬血细胞综合征早期实验室指标改变研究
2.
Retrospective analysis of clinical characteristics and factors affecting prognosis of 28 children with hemophagocytic syndrome
儿童噬血细胞综合征28例临床特点和预后分析
3.
Clinical characteristics of 68 children with hemophagocytic syndrome
儿童噬血细胞综合征68例临床研究
4) infection-associated hemophagocytic syndrome
感染相关性噬血细胞综合征
1.
Study on the value of the monitoring of the serum enzyme concentrations and the clinical significance of the changes of serum enzyme concentrations in children with infection-associated hemophagocytic syndrome;
儿童感染相关性噬血细胞综合征血清酶学的监测及临床意义
2.
Infection-associated hemophagocytic syndrome: Clinical case report;
感染相关性噬血细胞综合征的临床探讨
5) lymphoma-associated hemophagocytic syndrome
淋巴瘤相关噬血细胞综合征
6) macrophage activation syndrome
巨噬细胞活化综合征
1.
Four cases report of macrophage activation syndrome with systemic onset juvenile idiopathic arthritis in children;
幼年特发性关节炎全身型合并巨噬细胞活化综合征4例报告并文献复习
2.
Systemic lupus erythematosus and macrophage activation syndrome in children;
儿童期系统性红斑狼疮与巨噬细胞活化综合征
3.
Renal involvement appears to be of poor prognosis in systemic-onset juvenile idiopathic arthritis with macrophage activation syndrome.
幼年特发性关节炎全身型(SOJIA)合并巨噬细胞活化综合征(MAS)患儿出现严重肾脏损害,往往预后不良,早期、大剂量糖皮质激素单独或联合免疫抑制剂治疗,是决定预后的重要因素。
补充资料:Fanconi全血细胞减少综合征
Fanconi全血细胞减少综合征
为常染色体隐性遗传。表现:矮小占56%,头小占43%,拇指发育不全到缺如占78%。皮肤不均匀色素沉着,并有随年龄增长而增加的倾向,尤其在肛门生殖器,腹股沟,腋窝及躯干等。小阴茎、小睾丸和/或隐睾,占男性病人的44%。全血细胞减少是此病常见特征。发病时间可见于婴儿至二十几岁。骨髓广泛发育低下,其中可见造血灶,一些红细胞呈巨红细胞性。白细胞减少主要为粒细胞减少。尸解经常见到脾发育不全。染色体断裂多。常有感染发生。早期治疗可以延长生命。
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