1) Niemann-pick protein C1
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C型尼曼-匹克蛋白1
1.
Niemann-pick protein C1(NPC1) is a large integral membrane glycoprotein that resides in late endosomes,whereas niemann-pick protein C2(NPC2) is a small soluble protein found in the lumen of lysosomes.
然而,在C型尼曼-匹克病(N iemann-Pick d isease typeC,NPC)细胞中,胆固醇和糖鞘脂(glycosphingolip-ids,GSL)聚集在LE/LY中,这些物质从LE/LY转运到细胞内其它细胞器的速度非常缓慢,其原因在于NPC细胞中C型尼曼-匹克蛋白1(N iemann-pick protein C1,NPC1)或C型尼曼-匹克蛋白2(N iemann-pick protein C2,NPC2)发生基因突变。
2) Niemann-Pick C1 protein
![点击朗读](/dictall/images/read.gif)
C型1类尼曼-匹克蛋白
3) Niemann-pick protein C2
![点击朗读](/dictall/images/read.gif)
C型尼曼-匹克蛋白2
4) Niemann-Pick C2 protein
![点击朗读](/dictall/images/read.gif)
C型2类尼曼-匹克蛋白
5) niemann-pick type C1 like-1
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尼曼-匹克C1型类似蛋白1
6) Niemann-Pick disease type C
![点击朗读](/dictall/images/read.gif)
C型尼曼-匹克病
1.
Gliosis in the cerebellum of Niemann-Pick disease type C mice;
![点击朗读](/dictall/images/read.gif)
C型尼曼-匹克病小鼠小脑的胶质反应
2.
Changes in glial cells in the brain of mice with Niemann-Pick disease type C;
![点击朗读](/dictall/images/read.gif)
C型尼曼-匹克病小鼠脑内胶质细胞的变化
补充资料:匹克硫酸钠
分子式:C18H13NNa2O8S2.H2O
分子量:499.42
CAS号:10040-45-6
性质:
分子量:499.42
CAS号:10040-45-6
性质:
说明:补充资料仅用于学习参考,请勿用于其它任何用途。
参考词条