1) Cystic fibrosis
囊性纤维化
1.
The cystic fibrosis transmembrane conductance regulator(CFTR)is a chloride channel that belongs to the ATP-binding cassette(ABC)transporter superfamily.
囊性纤维化跨膜电导调节体(cystic fibrosis transmembrane conductance regulator,CFTR)是一种Cl~-通道,属ATP结合(ATP-binding cassette,ABC)转运体超家族。
2.
Mutation of CFTR which leads to cystic fibrosis will influence cell function.
囊性纤维化跨膜传导调节因子(CFTR)是一种重要的氯离子通道,突变易引起囊性纤维化病变,故得名。
3.
The etiology of CAVD is associated with the cystic fibrosis transmembrane conductance regulator(CFTR) gene and defects in the Wolffian duct, and frequently complicated by renal agenesis and other urogenital abnormalities.
研究表明 ,CAVD的发病与囊性纤维化跨膜转运调节物 (CFTR)基因突变和中肾管发育缺陷有关。
2) cystic fibrosis
囊纤维化
3) Huaweixian capsule
化维纤胶囊
1.
Determination of adenosine in Huaweixian capsule;
化维纤胶囊中腺苷含量的测定
4) fibrosis of seminal vesicle
精囊纤维化
5) PRSS1
胰腺囊性纤维化基因
1.
Objective Using multiple PCR to screen the mutational status of the protease serine 1(PRSS1) gene and serine protease inhibitor Kazal type1(SPINK1) gene in chronic pancreatitis.
目的探讨多重PCR技术在筛查慢性胰腺炎患者的易感基因即胰蛋白酶原基因(protease serine 1,PRSS1)和胰腺囊性纤维化基因(serine protease inhibitor Kazal type1,SPINK1)突变的情况。
6) water absorbent fibers/microencapsulation
吸湿性纤维/微胶囊化
补充资料：囊性纤维化的肝胆系病变
囊性纤维化的肝胆系病变
hepatic diseases in cystic fibrosis
囊性纤维化是常染色体隐性遗传的外分泌腺疾病，其主要见于肺、胰及肠道，可发生慢性阻塞性肺病、胰功能不全和肝硬化。其肝脏损害的病理特征：①叶间胆管内有浓缩的嗜酸物质；②汇管区纤维化伴有新生小胆管增生。可分三型：①局灶性胆汁性肝硬化有胆管增生；②胆管小支或其上皮有黏液，有增生、上皮化生及炎症；③汇管区纤维化但无胆管内黏液。本病国内罕见，美国发病率较高。儿童多见。婴儿期主要有持久性阻塞性黄疸，儿童及青年主要表现为肝硬化及门脉高压。常伴有肝脾大。可有小胆囊、胆囊功能减退、胆石、脂肪泻等。早期出现血清碱性磷酸酶同工酶增高和磺溴酞钠排出减少；汗液中氯化物增高，胰腺外分泌试验异常；结合肝活检可诊断。肺病变轻者出现门脉高压可行脾-肾静脉分流术；如肺功能差伴消化道出血，可用硬化剂注射治疗。
说明：补充资料仅用于学习参考，请勿用于其它任何用途。
参考词条